Tumefactive Brain Lesions in Patients with Neuromyelitis Optica Spectrum Disorder

Authors

  • Mahdi Barzegar Isfahan Neuroscience Research Center, Isfahan University of Medical Sciences, Isfahan, Iran
  • Nasim Nehzat Isfahan Neuroscience Research Center, Isfahan University of Medical Sciences, Isfahan, Iran
  • Navid Manouchehri Isfahan Neuroscience Research Center, Isfahan University of Medical Sciences, Isfahan, Iran
  • Omid Mirmosayeb Isfahan Neuroscience Research Center, Isfahan University of Medical Sciences, Isfahan, Iran
  • Vahid Shaygannejad Isfahan Neuroscience Research Center, Isfahan University of Medical Sciences, Isfahan, Iran
Abstract:

Background: Neuromyelitis Optica Spectrum Disorder (NMOSD) is an autoimmune neurological disorder that is characterized by optic neuritis and longitudinally-extended transverse myelitis lesions in spinal segments. Magnetic Resonance Imaging (MRI) findings are part of the diagnostic process in NMOSD patients, and abnormal lesion patterns may cause deviation from a correct diagnosis.  Clinical Presentation and Intervention: A 43-year-old female patient with abrupt cognitive loss, motor dysfunction and tumefactive spread of the demyelinating lesions in her brain presented to the Neurology Clinic of Kashani Hospital. Anti Aquaporine 4(AQP-4) antibody was observed, and the patient responded well to the NMOSD treatment.  Conclusion: NMOSD can be considered a differential diagnosis during an episode of Fulminant Demyelinating Disorder (FDD) with the tumefactive spread of the lesions.

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Journal title

volume 5  issue 2

pages  96- 100

publication date 2019-05

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